Case Report

The Successful Use of an Exchange Transfusion in a Child with Hereditary Spherocytosis Undergoing Congenital Cardiac Surgery

Oklahoma Children’s Hospital at OU Health, Oklahoma City, Oklahoma

Address correspondence to: Berkeley Stevens, CCP, MBA, Pediatric Perfusionist, Congenital Cardiac Surgery, Oklahoma Children’s Hospital, 8000 Stanton L Young Blvd., Oklahoma City 73104, Oklahoma. E-mail: This email address is being protected from spambots. You need JavaScript enabled to view it.

Received: 18 November 2020
Accepted: 31 March 2021

Abstract

Little is reported in the literature regarding hereditary spherocytosis (HS) and cardiopulmonary bypass (CPB). We present a case of a 19-month-old girl child who was referred for an atrioventricular septal defect (AVSD) and HS. The patient underwent surgical repair, and an exchange transfusion was performed at the initiation of CPB. No significant hemolysis or events attributed to HS were observed during or after CPB. The surgical repair of an AVSD in a pediatric patient with HS and total volume exchange transfusion is herein reported.