Case Report

Perfusion strategy and surgical repair of Type A interrupted aortic arch and Type 1 aortopulmonary window: a case report

University of Utah Health, Primary Children’s Hospital, Division of Cardiothoracic Surgery, Salt Lake City, UT, USA

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Received: 14 April 2025
Accepted: 2 September 2025

Abstract

Overview: Interrupted aortic arch in combination with an aortopulmonary window is an uncommon congenital cardiovascular defect. The anatomic separation between the aortic arch and descending aorta, combined with the communication between the ascending aorta and pulmonary trunk, leads us to a unique case where we can utilize the patient’s anatomic defect towards an efficient perfusion strategy. Description: The patient was a 19-day-old neonate who was initially discharged home after birth with no suspicion of congenital heart disease. The patient was later diagnosed with a type A aortic interruption with a large type 1 aortopulmonary window. Due to the unique combination of defects, surgery was accomplished utilizing single instead of dual aortic cannulation, and the repair was accomplished using a double patch technique. Comment: An individualized perfusion strategy was employed by taking advantage of the defect.